Aggressive Somatostatinoma, with Associated Pheocromocytoma in a Neurofibromatosis Patient

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Introduction: Neurofibromatosis is associated with a neuroendocrine phenotype as pheocromocytoma, primary hyperparathyroidism and gastropancreatic neuroendocrine tumors.

Aim(s): We present a case of a male patient with neurofibromatosis and several tumors simultaneously diagnosed.

Materials and methods: D.N., a 42-year-old male patient with a 15 yr history of mild arterial hypertension and neurofibromatosis, suffered an emergency duodenectomy for superior occlusion, caused by a tumor on the duodenum and the first jejune loop. Surgical exploration showed multiple metastasis of less than 1 cm into the peritoneum.

Conference: 8th Annual ENETSConcerence (2011)

Presenting Author:

Authors: Poiana C, Carsote M, Radoi V, Ene C, Gruia A,

Keywords: somatostatinoma, neurofibromatosis, pheocromocitoma, octreotidum,