Primitive Peripheral Neuroectodermal Tumor: Case Report


Introduction: Primitive neuroectodermal tumors belong to the family of Ewing sarcomatous tumors, all derived from the same stem cell. The cells of the neural crest are believed to be at the origin of these tumors. The predilection sites of these sarcomas are para-vertebral region, chest wall and the distal ends. The positive diagnosis of primary neuroectodermal tumors requires the contribution of histopathology, immunohistochemistry and cytogenetics.

Aim(s): In this study, we present a case report of a patient suffering from primitive peripheral neuroectodermal tumor

Materials and methods: The patient is a 20 years old female, without any particulars antecedents, exhibiting a swelling of the big toe of the right foot, of about 3cm on long axis thereof, encompassing and infiltrating the bone evolving after 4 months towards a beginning of necrosis and significant bleeding, a biopsy made was inconclusive.

Conference: 17th Annual ENETSConcerence (2020)

Presenting Author:

Authors: Ikram B, Soumeya G,

Keywords: Primitive neuroectodermal tumor, primary, peripheral, pPNET, CD99, surgery, chemotherapy,

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