Introduction: Neuroendocrine pancreatic tumors (pNET) are rare in young patients. They usually occur in the setting of genetic syndromes.
Aim(s): To report the clinical and pathological features of a young patient with pNET associated with cerebral neurofibroma.
Materials and methods: A 25-years old man with a long history of chronic abdominal pain and diarrhoea was observed in May 2006. A cerebral (right frontal) 1 cm lesion, stable in site, was known since 1996. A duodenal biopsy of a 2,5 cm lesion close to the papilla showed NE tissue. Octreoscan scintigraphy was positive in pancreatic head/duodenum. EUS confirmed a 3 cm pancreatic head mass infiltrating the duodenum with main duct dilation and stenosis of common bile duct. Exocrine pancreatic insufficiency with low fecal elastase (98ug/g) was present. At laparotomy was showen a jejunal invagination due to Meckel’s diverticulum and a pancreatic head lesion. A pancreaticoduodenectomy and Meckel resection were performed.
Conference: 12th Annual ENETS Conference 2015 (2015)
Category: Clinical cases/reports
Presenting Author: Doctor Valbona Lico
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