An Esophageal Gastrointestinal Stromal Tumor (GIST) in a Patient with MEN-1 Related Pancreatic Gastrinoma Abstract #426

Introduction: Both multiple endocrine neoplasia type 1 (MEN1)-related-gastrinomas and Gastrointestinal Stromal Tumors (GISTs) are rare neoplasms, and their association has been rarely reported.
Aim(s): We present a case of a man with an esophageal GIST and previously an MEN1-related pancreatic gastrinoma.
Materials and methods: The present report refers to a 44-year-old man who underwent surgical removal of a cephalo-pancreatic gastrinoma, peripancreatic lymph nodes and liver metastasis in April of 2004. The patient was then given long-term somatostatin analogs and diagnosed as having MEN-1 syndrome. The follow-up was uneventful until April 2009, when the patient reported a return of heartburn. The clinical assessment excluded a recurrence of gastrinoma, while upper gastrointestinal (GI) tract endoscopy findings were consistent with a narrowing of the distal third of the esophagus.
Conference: 9th Annual ENETS Conference (2012)
Category: Clinical
Presenting Author: Dr Roberta E Rossi

To read results and conclusion, please login ...

Further abstracts you may be interested in

#349 Gastrointestinal Stromal Tumor (GIST) Of The Esophagus In A Patient With MEN-1 And-Related Pancreatic Gastrinoma
Introduction: Both Multiple Endocrine Neoplasia type 1 (MEN-1; OMIM #613733)-related-gastrinomas and Gastrointestinal Stromal Tumors (GISTs; OMIM #606764) are rare neoplasms and their association has been rarely reported so far.
Conference:
Category: Basic
Presenting Author: Dr Roberta E Rossi
#615 Gastrinoma and Neurofibromatosis Type 2: Is There an Association?
Introduction: Gastroenteropancreatic neuroendocrine tumors have been seldom described in association with neurofibromatosis type-1, whereas an association with neurofibromatosis type-2 (NF2) has never been reported.
Conference: 10th Annual ENETS Conference 2013 (2013)
Category: Epidemiology/Natural history/Prognosis - Descriptive epidemiology
Presenting Author: Dr Roberta E Rossi
#1785 Eterogeneity of Duodenal Neuroendocrine Tumors: A Multi-Centre Experience in Italy
Introduction: Duodenal neuroendocrine neoplasms (dNENs) are heterogeneous tumors, which could have a highly variable prognosis.
Conference: 14th Annual ENETS conference 2017 (2017)
Category: Epidemiology/Natural history/Prognosis - Prognosis
Presenting Author: dr Sara Massironi
#2138 Eterogeneity of Duodenal Neuroendocrine Tumors: A Multi-Centre Experience In Italy
Introduction: The optimal management of duodenal neuroendocrine neoplasms (dNENs) is unclear and endoscopic resection is increasingly performed instead of surgery.
Conference: 15th Annual ENETS conference 2018 (2018)
Category: Epidemiology/Natural history/Prognosis- Registries, nationwide and regional surveys
Presenting Author: MD Roberta Elisa Rossi
#2691 Somatostatin Analogs in Patients with Zollinger Ellison Syndrome (ZES): An Observational Study
Introduction: Zollinger Ellison syndrome (ZES) is a rare syndrome caused by gastrin hypersecretion from a primary neuroendocrine tumor (NET), usually located within the duodenum or into the pancreas. Gastrinomas have two important treatment goal: the control of the gastrin-excess state and the control of tumor growth.
Conference: 17th Annual ENETS Conference 2020 (2020)
Category: Medical treatment - Chemotherapy Somatostatin analogues, Interferon
Presenting Author: dr Sara Massironi