Challenges in the Management of a Disseminated Malignant Abdominal Paragangliom (MPGL) Abstract #400

Introduction: Despite current availability of large array of Rx modalities, management of MPGLs still pose a challenge.
Aim(s): Mutomodal Rx including surgery, radioablation, Octreotide and 1-131 MIGB failed to arrest progression of MPGL. Refinements in disseminated PGLs are needed.
Materials and methods: A 20-year-old asymptomatic male was referred with a 3-yr. history of large skull occipital and abdominal masses. Imaging studies: Whole body CT, MIBG/Octreoscans, abdominal angiogram, serum and urinary catecholamies, Serum CGA, Genetic study for SHDB/C/D, VHL, RET were done.
Conference: 9th Annual ENETS Conference (2012)
Category: Clinical
Presenting Author: Dr. Mohammed Ahmed

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