Characteristics and Management of Paragangliomas, 10 Years Experience Abstract #2972

Introduction: Paraganglioma (PG) is a rare extra-adrenal neuroendocrine tumor, with common sites of presentation being abdomen, and head and neck region. The majority of PGs appear to be sporadic. However, almost half of cases are associated with an inherited syndrome. The highest malignancy rates are seen in paragangliomas (PGs) associated with SDHB mutations, which are usually abdominal and secretory.
Aim(s): In this research, we have investigated the characteristics and outcomes in a series of PGs.
Materials and methods: In this retrospective, single-institution study, all paraganglioma patients diagnosed between 2010 and 2019 were reviewed. We recorded baseline clinical-pathological-genetic characteristics and overall survival (OS).
Conference: 17th Annual ENETS Conference 2020 (2020)
Category: Epidemiology/Natural history/Prognosis - Registries, nationwide and regional surveys
Presenting Author: MD Emilia Sardo

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