Ectopic hormone secreting phaeochromocytoma: A francophone observational study Abstract #125

Introduction: Ectopic hormone-secreting phaeochromocytomas are rare and only small reports of 1-2 cases exist in the literature. In the past, this condition has been linked with increased malignancy, familial syndromes and ACTH secretion.
Aim(s): We wanted to test these hypotheses and shed light on the nature of ectopic hormone-secreting phaeochromocytomas.
Materials and methods: This is a multi-center (francophone) observational study. Inclusion was based upon abnormal pre-operative hormone tests in patients with phaeochromocytoma that normalized after removal of the tumor. Where possible, immunohistochemistry was performed to confirm that secretion came from the tumor.
Conference: 7th Annual ENETS Conference (2010)
Category: Clinical
Presenting Author: Prof Bruno Carnaille

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