Extrapulmonary Small Cell Neuroendocrine Carcinoma of the Colon in an 18-Year-Old Girl Abstract #855

Introduction: Extrapulmonary small cell carcinoma (EPSCC) is a very rare aggressive malignant tumor typical for older age. Prognosis of EPSCC remains very poor, with three years OS 38% and five years OS less than 13%. The median survival for GI localised EPSCC is only five months. Initial extent of disease is the most sensitive prognostic factor.
Aim(s): Case study of a very rare tumor with extremely agressive behavior in an unusually young patient.
Materials and methods: Eighteen-year-old girl with one week history of abdominal pain was admitted to the hospital with acute hepato-renal failure and severe hypercalcaemia. US/MRI showed extreme hepatomegaly and multiple small nodules in liver parenchyma. Within 48 hours she suddenly developed hemorrhagic shock with intrabdominal bleeding. Laparotomy revealed spontaneous rupture of the right liver lobe. Days after surgery there were complications, including multiple organ failure and coagulopathy. Despite intensive care, the girl died only 20 days after the first symptoms occur.
Conference: 11th Annual ENETS Conference (2014)
Category: Clinical cases/reports
Presenting Author: MD, PhD Viera - Bajciova

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