Insulinomas in Children Abstract #403

Introduction: Insulinomas are extremely rare tumors in children and an uncommon first manifestation of MEN1 syndrome. Insulinomas are usually benign tumors with only a few reports of malignant cases in children.
Aim(s): To investigate the morphological and genetic characteristics of Russian children with primary insulinomas.
Materials and methods: Insulinoma was diagnosed biochemically and by imaging and was verified histopathologically. Sequencing of the MEN1 gene was performed and families of the mutation carriers were studied. Follow-up included screening for signs of MEN1 and metastases in case of malignant tumors.
Conference: 9th Annual ENETS Conference (2012)
Category: Clinical
Presenting Author: MD Maria Melikian
Keywords: MEN-1

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