Primary Hepatic Neuroendocrine Tumors: Four Familial Case Series with Review of Literature Abstract #883

Introduction: Non-multiple endocrine neoplasia (MEN) familial neuroendocrine tumors (NET) are very rare with only six families being described to date. Primary hepatic neuroendocrine tumors (PHNETs) are rare tumors with a particular sporadic diagnosis. Herein, we report a series of four members of one Lebanese family, diagnosed with primary hepatic neuroendocrine tumors.
Aim(s): We present four well-documented cases of primary hepatic neuroendocrine tumors with review of the literature and a focus on genetic studies.
Materials and methods: We recently collected four Lebanese family members who were separately diagnosed with hepatic masses: the daughter at the age of 16 years and her mother at the age of 43 years, the maternal cousin at the age of 25 years and his mother at the age of 53 years. All four patients underwent partial hepatectomy at different times.
Conference: 11th Annual ENETS Conference (2014)
Category: Clinical cases/reports
Presenting Author: Dr Rita E Assi

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