Challenges in the Management of VIPoma Patients

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Introduction: VIPomas are a rare neuroendocrine tumor (NET). 90% are pancreatic. 40-70% are metastatic at presentation. The VIPoma syndrome is characterized by secretory diarrhoea, hypokalaemia and achlorhydria.

Aim(s): To review the complexities of management and outcome in a case series of six VIPoma patients with long-term follow-up.

Materials and methods: A retrospective study of six VIPoma patients (two male, four female; age 33-72 years at presentation) was performed. Diagnosis was based on the presence of compatible symptoms, plasma VIP levels, imaging and histopathology. Clinical management and course was reviewed. Follow-up was complete in all patients (range 72 – 168 months, median 84 months).

Conference: 8th Annual ENETSConcerence (2011)

Presenting Author:

Authors: El-Khouly F, Khan M, Toumpanakis C, Meyer T, Caplin M,

Keywords: VIPoma, VIPoma syndrome,