Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia (DIPNECH): Characterisation of Prevalence and Prognosis in the Pulmonary Carcinoid Population Abstract #2246

Introduction: DIPNECH is considered a rare condition and the natural history is poorly described. It is thought to give rise to pulmonary carcinoids (PCs) (>5mm) or tumourlets (≤5mm).
Aim(s): We aimed to assess the prevalence and characteristics of DIPNECH in the PC population and to investigate predictors of progression-free (PFS) and overall survival (OS).
Materials and methods: We identified patients with PCs and histologically-proven DIPNECH and/or high suspicion of DIPNECH on imaging. Relationship between baseline characteristics and PFS and OS was analysed using the Kaplan-Meier method and curves were compared using the logrank test.
Conference: 15th Annual ENETS conference (2018)
Category: Epidemiology/Natural history/Prognosis- Registries, nationwide and regional surveys
Presenting Author: Dr Aimee Hayes

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Authors: Cui T, Elgue G, Li S C, Hurtig M, ...
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