Abstract Library

#2255 When Is Right Hemicolectomy Really Indicated for Pediatric Appendiceal NETs?

Introduction: Pediatric NET of the appendix (ANET) are rare tumors with unknown real incidence.For pediatric age initial staging procedures are not standardized and guidelines for pediatric patients with ANET do not exist.

Conference: 15th Annual ENETSConcerence (2018)

Presenting Author:

Authors: Bajciova V, Tuma J, Jezova M,

Keywords: Right hemicolectomy, appendix, predictive factors, pediatric age,

#1536 Merkel Cell Carcinoma – Epidemiology Data from the Czech National Cancer Registry

Introduction: Merkel cell carcinoma (MCC) is rare and aggressive neuroendocrine tumor. The incidence is increasing worldwide, most probably due to population aging (mostly in the Western Europe), higher rates of sun exposure, immunosuppression and other not well defined epigenetic changes.

Conference: 13th Annual ENETSConcerence (2016)

Presenting Author: Bajciova V

Authors: Bajciova V, Barkmanová J, Zvolsky M, Sedlackova E,

Keywords: Merkel cell carcinoma, register, epidemiology, ,

#944 Pheochromocytoma and Paraganglioma in Pediatric Age

Introduction: Pheochromocytoma (PHE) and paraganglioma (PGL) are rare tumors of the adrenal medulla and extra-adrenal sympathetic chromaffin tissue. Nearly 30% of them are familiar or associated with genetic syndromes (VHL, MEN2, NF1, SDH mutation, Pacak-Zhuang). Only 20% PHE occur before 20 years of age. Incidence of pediatric PHE is 0.3:1 million.

Conference: 11th Annual ENETSConcerence (2014)

Presenting Author: Bajciova V

Authors: Bajciova V, Kren L, Vicha A,

Keywords: pheochromocytoma, paraganglioma, pediatric age,

#855 Extrapulmonary Small Cell Neuroendocrine Carcinoma of the Colon in an 18-Year-Old Girl

Introduction: Extrapulmonary small cell carcinoma (EPSCC) is a very rare aggressive malignant tumor typical for older age. Prognosis of EPSCC remains very poor, with three years OS 38% and five years OS less than 13%. The median survival for GI localised EPSCC is only five months. Initial extent of disease is the most sensitive prognostic factor.

Conference: 11th Annual ENETSConcerence (2014)

Presenting Author: Bajciova V

Authors: Bajciova V, Kren L, Oltova A,

Keywords: colon EPSCC, young age,

#652 Neuroendocrine Neoplasms in Childhood and Adolescents

Introduction: NEN are very rare tumors in children and adolescents with predominance in adolescent girls. The annual incidence is about 1.14:1 million. The most frequent localization is appendix. Bronchial NEN, even extremly rare, is the most frequent primary epithelial lung tumor in children.

Conference: 10th Annual ENETSConcerence (2013)

Presenting Author: Bajciova V

Authors: Bajciova V, Tuma J, Kren L, Prasek J,

Keywords: NEN in childhood and adolescents, incidence, localization, treatment, outcome,