Abstract Library

#102 Presentation and outcome of pancreaticoduodenal tumors in Multiple Endocrine Neoplasia type 1 (MEN 1) syndrome

Introduction: Multiple endocrine neoplasia type 1 (MEN 1) is a rare autosomal dominant condition characterized by the development of parathyroid, pancreaticoduodenal endocrine and pituitaty tumors. Pancreaticduodenal endocrine tumors (PDETs) are a frequent manifestation of MEN 1, with a prevalence ranging from 30 to 75%, and represent a major cause of death in one-third of patients. There is continuing debate on their management, mainly on the optimal surgical strategy, due to their multicentricity and high recurrence rate.

Conference: 7th Annual ENETSConcerence (2010)

Presenting Author:

Authors: Davi' M, Boninsegna L, Toaiari M, Scarpa A, Francia G,

Keywords: pancreaticoduodenal endocrine tumors, MEN 1,