Clinical response to somatostatin analogues in patients with DIPNECH: Findings from a new longitudinal registry

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Introduction: Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia (DIPNECH) often presents with symptoms of cough and dyspnoea. DIPNECH remains understudied, and response to somatostatin analogues (SSAs) has been reported in a few small series.

Aim(s): Response to SSA treatment in patients with DIPNECH remains poorly understood. This registry aims to provide real-world epidemiological and clinical evidence for SSA treatment in patients with DIPNECH.

Materials and methods: After IRB approval, adult patients with DIPNECH were identified. Demographics, symptoms, pathology, radiographic characteristics, treatments, and outcomes were collected. Data analysis was conducted using R.

Conference:

Presenting Author: Libre M

Authors: Libre M, Skotte E, Linden A, Wu J, Lippincott E,

Keywords: DIPNECH, somatostatin analogue,