Neuroendocrine Pancreatic Tumor Associated with a Cerebral Neurofibroma. A Case Report.

#1055

Introduction: Neuroendocrine pancreatic tumors (pNET) are rare in young patients. They usually occur in the setting of genetic syndromes.

Aim(s): To report the clinical and pathological features of a young patient with pNET associated with cerebral neurofibroma.

Materials and methods: A 25-years old man with a long history of chronic abdominal pain and diarrhoea was observed in May 2006. A cerebral (right frontal) 1 cm lesion, stable in site, was known since 1996. A duodenal biopsy of a 2,5 cm lesion close to the papilla showed NE tissue. Octreoscan scintigraphy was positive in pancreatic head/duodenum. EUS confirmed a 3 cm pancreatic head mass infiltrating the duodenum with main duct dilation and stenosis of common bile duct. Exocrine pancreatic insufficiency with low fecal elastase (98ug/g) was present. At laparotomy was showen a jejunal invagination due to Meckel’s diverticulum and a pancreatic head lesion. A pancreaticoduodenectomy and Meckel resection were performed.

Conference: 12th Annual ENETSConcerence (2015)

Presenting Author: Lico V

Authors: Moletta L, Milanetto A, Lico V, Farinati F, Alaggio R,

Keywords: pnet, cerebral neurofibroma, nf-1,

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