Non-functional retroperitoneal paraganglioma in a young patient: A case report

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Introduction: Paragangliomas are neuroendocrine tumours arising in the parasympathetic nervous system, outside the adrenal gland. Retroperitoneal location is extremely rare. Non-functional paragangliomas often represent a diagnostic challenge.

Aim(s): Retroperitoneal paragangliomas are extremely rare and carry a poor prognosis. Non-functioning tumours are usually diagnosed by imaging and biopsy, the gold standard. Treatment usually involves surgical excision, and there is no evidence of efficacy of adjuvant therapy.

Materials and methods: We report the case of a 21-year-old patient who consulted for abdominal pain showed a retroperitoneal latero-aortic tumour. Histopathological and immunohistochemistry examinations after complete surgical resection confirmed the diagnosis of paraganglioma, which was chromogranin A and synaptophysin positive. No adjuvant treatment had been received since there is no consensus on its usefulness.

Conference:

Presenting Author:

Authors: Aris H, Saidi M, Lahfa I,

Keywords: retroperitoneal paraganglioma, surgery, monitoring,