38 Years of Experience in a Single Centre on Neuroendocrine Pancreatico-Duodenal Tumors in Multiple Endocrine Neoplasia Type 1 Syndrome

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Introduction: Multiple Endocrine Neoplasia type 1 (MEN1) syndrome has an autosomal dominant transmission. Combination of tumors: parathyroid, pituitary and pancreatico-duodenal (PD) NETs. PD NETs in MEN1 syndrome show propensity for malignant degeneration.

Aim(s): We evaluated occurrence of PD, therapeutic strategies and follow up (FU) of PD NETs in MEN1 patients observed in our Unit.

Materials and methods: From 1975 to 2013: 322 PD NETs, 40/322 had a MEN1 syndrome. Average 40.5 years (range 13-69 yrs), 20 M/20 F. Only patients with MEN1 syndrome and a PD NET diagnosed by imaging or histology were included. FU to December 2013

Conference: 12th Annual ENETSConcerence (2015)

Presenting Author: Milanetto A

Authors: Milanetto A, Lico V, Alaggio R, Martini C, Pedrazzoli S,

Keywords: net, men1 syndrome, pancreatic tumor.,