Demystifying DIPNECH: Updates from a new longitudinal patient registry

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Introduction: Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia (DIPNECH) was first characterised in 1992 with a case series describing 6 patients with neuroendocrine cell hyperplasia, with cough and dyspnoea. Since that time, DIPNECH has remained understudied.

Aim(s): While rare, DIPNECH is possibly more common than the literature reflects. We hope to characterise the clinical characteristics and potential treatments by developing a longitudinal registry.

Materials and methods: After IRB approval, we identified adult patients with DIPNECH at Vanderbilt-Ingram Cancer Center. Demographics, symptoms, pathology, radiographic characteristics, treatments, and outcomes were collected. Data analysis was conducted with R.

Conference:

Presenting Author:

Authors: Skotte E, Linden A, Libre M, Lippincott E, Cass A,

Keywords: DIPNECH,