Gastrointestinal Stromal Tumor (GIST) Of The Esophagus In A Patient With MEN-1 And-Related Pancreatic Gastrinoma

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Introduction: Both Multiple Endocrine Neoplasia type 1 (MEN-1; OMIM #613733)-related-gastrinomas and Gastrointestinal Stromal Tumors (GISTs; OMIM #606764) are rare neoplasms and their association has been rarely reported so far.

Aim(s): Present report refer to a 44-year-old-man who had undergone in April 2004 surgical removal of cephalo-pancreatic gastrinoma, peri-pancreatic lymph nodes and liver metastasis.

Materials and methods: The patient was then referred to our Gastroenterology Unit, given long term somatostatin analogues and diagnosed as having MEN-1 syndrome. Follow up was uneventful up to April 2009, when patient referred renewal of diarrhea and heartburn.

Conference:

Presenting Author:

Authors: Rossi R, Massironi S, Ferrero S, Spampatti M, Conte D,

Keywords: Gastrointestinal Stromal Tumors (GISTs); Neuroendocrine Tumor (NETs); Multiple Endocrine Neoplasia type 1 (MEN-1) syndrome; Gastrinoma,