Abstract Library

#4608 A complex and rare association of neuroendocrine and endocrine neoplasms: A case report

Introduction: Neuroendocrine tumours (NETs) are sporadic or genetically inherited heterogenous neoplasms affecting multiple sites.

Conference:

Presenting Author: Cerroni L

Authors: Cerroni L, Filice A, Feola T, Sesti F, Vincenzi L,

Keywords: cushing disease, atypical carcinoid, ileal net, genetics,

#4479 Bilateral adrenal masses associated with arterial hypertension with rare and unexpected definitive histopathological diagnosis: A case report

Introduction: During the clinical approach of bilateral adrenal masses, some imaging, biochemical and clinical guidelines are established to guide the diagnosis; however, only the histopathological result is what definitively establishes the diagnosis.

Conference:

Presenting Author: Rueda M

Authors: Rueda M, Cuellar A, Tapiero-Garcia M,

Keywords: adrenal gland, adrenal mass, Cystic lymphangioma, endothelial cyst, systemic arterial hypertension,

#3842 Long response to 177-Lu DOTATATE of a long malignant metastatic pheochromocytoma survivor

Introduction: A 64-year-old man was admitted on November 2010 with a CT-scan showing a 9cm right adrenal mass and high 24-hour urine metanephrins and cathecolamins. The mass was resected in December 2010 confirming a pT3N1 pheochromocytoma (PHEO). In May 2013 he presented a local recurrence that was resected proving metastatic lymphatic tissue. On May 2014 biochemical progression preceded a CT scan showing retroperitoneal lymphadenophaties with MIBG uptake. He was then treated with 131I-MIBG (two cycles) until May 2015, having biochemical and radiological response. After lymphatic tumor progression in January 2018, he received two more cycles of 131I-MIBG therapy (cumulative dose 800mCi) with proven refractory disease. He continued follow-up until two new abdominal masses appeared in October 2020. A high uptake in the 99Tc octreotide scintigraphy showed somatostatin receptors expression. The patient refused to participate in a clinical trial, so he was treated off-label with 177Lu-DOTATATE (800mCi) four doses from February to July 2021 achieving a near-complete response.

Conference:

Presenting Author: Martin Fernandez de Soignie A

Authors: Martin Fernandez de Soignie A, Martinez Moreno E, Antón-Pascual B, Pantin Gonzalez C, Sanchez Baños N,

Keywords: pheochromocytoma, 177-Lutetium,

#1414 Non-functioning Adrenal Composite Pheochromocytoma-Ganglioneuroma Simultaneous with Subclinical Cushing's Syndrome Due to Contralateral Adrenal Hyperplasia - An Unusual Presentation

Introduction: “Composite” pheochromocytoma is a rare tumor, consisting of pheochromocytoma and neuroblastic tumors. The definite diagnosis is histological. Subclinical Cushing's syndrome refers to autonomous glucocorticoid production without specific signs and symptoms of Cushing's syndrome.

Conference: 13th Annual ENETSConcerence (2016)

Presenting Author: Kiraly A

Authors: Kiraly A, Muntean V, Domsa I, Ghervan C,

Keywords: adrenal, composite, pheochromocytoma, ganglioneuroma, hypercorticism.,

#716 Adrenal Metastases and Neuroendocrine Breast Carcinoma in a MEN-1 Patient

Introduction: In Multiple Endocrine Neoplasia type 1 (MEN-1) pituitary, parathyroid and pancreatic/duodenal endocrine cells are typically involved. Other neoplasms also occur.

Conference: 10th Annual ENETSConcerence (2013)

Presenting Author: Pasquali C

Authors: Moletta L, Milanetto A, Sperti C, Alaggio R, Pedrazzoli S,

Keywords: MEN-1 syndrome, breast cancer, adrenal metastasis, rare tumors,