Abstract Library

#2255 When Is Right Hemicolectomy Really Indicated for Pediatric Appendiceal NETs?

Introduction: Pediatric NET of the appendix (ANET) are rare tumors with unknown real incidence.For pediatric age initial staging procedures are not standardized and guidelines for pediatric patients with ANET do not exist.

Conference: 15th Annual ENETSConcerence (2018)

Presenting Author:

Authors: Bajciova V, Tuma J, Jezova M,

Keywords: Right hemicolectomy, appendix, predictive factors, pediatric age,

#944 Pheochromocytoma and Paraganglioma in Pediatric Age

Introduction: Pheochromocytoma (PHE) and paraganglioma (PGL) are rare tumors of the adrenal medulla and extra-adrenal sympathetic chromaffin tissue. Nearly 30% of them are familiar or associated with genetic syndromes (VHL, MEN2, NF1, SDH mutation, Pacak-Zhuang). Only 20% PHE occur before 20 years of age. Incidence of pediatric PHE is 0.3:1 million.

Conference: 11th Annual ENETSConcerence (2014)

Presenting Author: Bajciova V

Authors: Bajciova V, Kren L, Vicha A,

Keywords: pheochromocytoma, paraganglioma, pediatric age,

#634 Merkel Cell Carcinoma in a Nine-Year-Old Girl

Introduction: Merkel cell carcinoma (MCC) of the skin is a rare neuroendocrine tumor characterized by its rapid growth and aggressive clinical behavior. MCC is a typical tumor of older age (average age is 65 years). In children and adolescents less than 20 years of age, it is extremely rare. Information regarding MCC in childhood can be found in the literature only in the form of individual case reports. Due to the rarity of MCC in the young population, any clinical studies or treatment recommendations in these patients are missing.

Conference: 10th Annual ENETSConcerence (2013)

Presenting Author: Bajciova V

Authors: Bajciova V, Kren L, Sterba J, Prasek J,

Keywords: Merkel cell carcinoma, pediatric age, rarity, effective treatment,