#3241
Clinical features and management of paragangliomas in a tertiary university hospital
Introduction:
Paragangliomas (PG) are rare neuroendocrine tumors that arise from the extra-adrenal paraganglia. The most frequent location is head and neck PG (HNPG), usually non-functioning tumors. PG present a high rate of genetic susceptibility mainly associated with SDHx mutation. Clinical presentation depends upon catecholamine secretion and tumor location. Surgery remains the standard treatment, although radiotherapy and systemic therapies can be considered for unresectable or metastatic disease.
Conference:
18th Annual ENETS Concerence (2021)
Presenting Author:
Authors:
Damaso S,
Lopes Brás R,
Paiva R,
Macedo D,
Fernandes I,
Keywords:
paraganglioma,
treatment,
sdhb gene,